A Case of the TOF with Absent Pulmonary Valve Syndrome compl
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Introduction
Absent pulmonary valve syndrome is a rare congenital heart disease with severe pulmonary insufficiency, characterized with aneurysmal dilation in the pulmonary artery and one or both of its branches, along with a rudimentary or dysplastic pulmonary valve. Absence of pulmonary valve may accompany ventricular septal defect, or it may be together with intact ventricular septum and tricuspid atresia. It is different from TOF regarding its clinical findings and course and hemodynamic features. The abnormal dilation in the pulmonary artery (PA) causes compression against the tracheobronchial tree, which can lead to extensive bronchomalacia or other various pulmonary complications. In this paper, we present a case of Fallot type APVS diagnosed in antenatal period which ended up with early neonatal death.....

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4992531/
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