A rare type of persistent fetal vasculature
Persistent fetal vasculature (PFV) is a rare congenital developmental malformation of the eye. It is caused by the incomplete regression of the fetal hyaloid vasculature. Persistent fetal vasculature, previously referred to as persistent hyperplastic primary vitreous (PHPV), is usually characterized by microphthalmia, a shallow anterior chamber, elongated ciliary processes, a posterior subcapsular cataract and a fibrovascular stalk that extends from the optic disc to the lens.

This paper, published in the Journal Ophthalmology Case Reports, describes a case of a 7-year old who presented with a history of poor vision on the right eye. On ophthalmologic examination, no light perception was noted in the affected eye. Slit-lamp findings for both eyes were unremarkable. There was no note of microphthalmia, shallow anterior chamber nor was there a subcapsular cataract.

On dilated funduscopy of the affected eye, a fibrovascular stalk was seen emanating from the optic nerve. This was further documented with ocular ultrasound. Based on the clinical findings, a diagnosis of persistent fetal vasculature, posterior type, was made. Since the affected eye had no visual potential, a conservative mode of management was instituted.

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