A retinopathy in young patient with co-inheritance of hetero
The retinopathy is an uncommon complication in individuals with sickle cell trait except for the cases of sickle cell trait associated with systemic arterial hypertension, diabetes mellitus, syphilis, tuberculosis and sarcoidosis.

Case Presentation

A 16-year-old Caucasian patient with no known past medical history presented with 2 years of blurry vision in the right eye. He had no other ocular, medical, or surgical history. He rarely sought medical care and was on no medications. His mother has Sickle cell anaemia (Hb SS). In December 2013, he consulted an ophthalmologist for a history of sudden onset of amaurosis (Transient monocular visual loss) in the right eye associated with headaches and dizziness. Dilated fundus examination found unilateral papilledema in the left eye without loss of visual acuity. In the interpretation of Humphrey visual field testing, it has been reported that the right visual field showed some scotomas. The color vision examination was normal. Fundus fluorescein angiography (FFA) of the right eye revealed temporal capillary non-perfusion corresponding to retinal ischemia with no neovascularization. FFA of the left eye showed venous tortuosity with no visible ischemic areas. The retinopathy in the right eye was treated successively with scattered argon laser photocoagulation. There was no diagnosis of intracranial tumor, the magnetic resonance imaging and the brain computed tomography were normal.

http://bmcophthalmol.biomedcentral.com/articles/10.1186/s12886-017-0402-x
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