Atypical Cardiopulmonary Manifestations in Pediatric Behcet'
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Behcet's disease (BD) is a multisystem auto inflammatory disease of unknown etiology. Cardiopulmonary involvement is rare, especially in young patients, and carries high morbidity and mortality rates. Of 26 patients with pediatric BD enlisted,three patients with severe atypical cardiorespiratory presentations were encountered .

Three adolescents presented with intracardiac thrombi and left anterior descending (LAD) obstruction causing myocardial infarction, pulmonary artery aneurysm with pulmonary embolism (PE) in situ, and suspected epiglottitis. Two patients had a delayed diagnosis of BD, and all had good response to anti?inflammatory agents.

This study demonstrated that pediatric BD is associated with atypical cardiopulmonary manifestations which may be life?threatening. Since diagnosis may be challenging, a high index of suspicion is needed especially in young patients, to promptly diagnose and treat these complications. Cardiopulmonary signs and symptoms, though uncommon, may be the first manifestation and a clue to the diagnosis of this rare disease.

source: https://onlinelibrary.wiley.com/doi/abs/10.1002/ppul.25068?af=R
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