Dental Mx of a Child with Dentinogenesis Imperfecta
Dentinogenesis imperfecta (DI) is a hereditary dentin defect caused by an autosomal dominant mutation in dentin sialophosphoprotein gene.

Defective dentin development results in discolored teeth that are prone to wear and fracture. Early diagnosis and proper treatment are necessary to achieve better functional and esthetic results and minimize nutritional deficiencies and psychosocial distress.

In order to prevent excessive loss of tooth structure, placement of stainless steel crowns (SSCs) on deciduous and young permanent posterior teeth is recommended as soon as such teeth erupt. This clinical report, published in the Journal of Dentistry of Tehran University of Medical Sciences presents the clinical manifestations and management of a 3.5-year-old child diagnosed with DI type II.

A three-and-a-half-year-old male patient presented with the complaint of brown discoloration of his teeth and excessive decay of his primary teeth. The patient also complained of intermittent pain in the lower right posterior region for the past one month. His primary dentition was grayish brown in color and had a translucent hue.

Teeth were small in size and showed excessive decay, with complete loss of enamel in most teeth. Coronal height of the teeth was reduced to one-third of the normal. Exposed dentin was visible in incisors, canines, first molars, and the right mandibular second molar.

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