Idiopathic Lymphoid Interstitial Pneumonia
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Idiopathic Lymphoid Interstitial Pneumonia (LIP) is considered to be a rare interstitial lung disease. The initial American Thoracic Society/European Respiratory Society (ATS/ERS) International multidisciplinary consensus paper on Idiopathic Interstitial Pneumonia of 2002, LIP was classified as one of the seven major idiopathic interstitial lung diseases. Since the first description of LIP in 1969, so far only 14 biopsy proven cases of idiopathic LIP have been described in the literature. The clinical course is reported to be highly variable in this rare form of interstitial pneumonia.

Case Report

74 years old male diagnosed was referred to specialized respiratory diseases unit with worsening dyspnoea. His NYHA (New York Heart Association) dyspnoea score worsened from grade I to grade IV during a period of three months. He did not have cough or constitutional symptoms such as night sweats or loss of weight. He gave a history of 3 pack years of smoking, stopped 20 years ago. He did not have clinical features suggestive of connective tissue diseases, chronic liver cell diseases or any hematological diseases. There was no history of known exposures to organic or inorganic dusts.

On examination he was dyspnoeic at rest with a SPO2 of 82% on air. He had grade II finger clubbing. There was no plethora, lymphadenopathy, inflamed or deformed joints or skin manifestations of connective tissue disorders. His respiratory rate was 22 breaths per minute and auscultation revealed bilateral basal fine end inspiratory crepitations.....