A one-month-old male infant presented to us with progressive right maxillary swelling and alveolar fullness, first noted at 6 days of age. The child was born term, and had no significant perinatal history. No functional deficits due to maxillary mass were reported. Computed tomography (CT) revealed a heterogeneous, mildly enhancing and expansile lesion of the right maxilla, replacing the right maxillary sinus and alveolar ridge. Orbital contents were normal.