Ischemic fasciitis of the left buttock with BPAN
Ischemic fasciitis is a rare condition that occurs in debilitated and immobilized individuals, usually overlying bony protuberances. Because the histology shows a pseudosarcomatous proliferation of atypical fibroblasts, and because the lesion can increase in size, ischemic fasciitis can mimic sarcoma.

Beta-propeller protein-associated neurodegeneration (BPAN) arises in infancy and results in progressive symptoms of dystonia, Parkinsonism, and dementia once the individual reaches adolescence or early adulthood, and is usually fatal before old age. Published in the American Journal of Case Reports, a case of ischemic fasciitis of the buttock is presented in an adult woman with BPAN.

A 40-year-old woman with BPAN and symptoms of mental and physical deterioration, had become increasingly wheelchair-dependent and presented with a mass in her buttock that had been increasing in size for two months. CT imaging showed an ill-defined subcutaneous lesion between the dermis and the gluteal muscle, which was suspicious for malignancy.

A needle biopsy of the mass was performed. The histology examination showed benign ischemic fasciitis. A follow-up CT scan performed 3.5 months after identification of the lesion showed that it had decreased in size.

Learning Points:-
• Because BPAN is a neurodegenerative disease that can cause immobility, a history of BPAN in patients of all ages may be associated with an increased risk of developing ischemic fasciitis.

• The correct diagnosis is essential, as ischemic fasciitis, although benign, can mimic malignancy.

Read more here: https://pxmd.co/fyLkx
Like
Comment
Share