Multiply recurrent solitary fibrous tumor of the orbit witho
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Solitary fibrous tumor (SFT) is a rare mesenchymal spindle cell neoplasm originally described in the pleura and subsequently identified in a number of extrathoracic sites. Orbital SFT was first described in 1994; since then, more than 100 cases have been reported or reclassified with that diagnosis. Only 4 patients were younger than 10 years when first diagnosed as having orbital SFT. While most reports describe a benign clinical course, rare cases of primary malignant orbital SFT have also been documented. Increased cellular atypia or mitotic activity in recurrent lesions following primary excision of orbital SFTs has also been described, suggesting that complete initial resection is a critical prognostic factor in preventing malignant degeneration. We describe a patient with orbital SFT whose proptosis was first recognized at age 9 years and who underwent surgical excision at various institutions at ages 12, 22, and 52 years.

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