Pigmented paravenous retinochoroidal atrophy
The present case has been reported in the Indian Journal of Opthalmology.

A 24-year-old female presented with complaint of diminution of vision in both eyes (OU) for 1 year, with no past history of inflammation, trauma, or nyctalopia and no family history of retinal disorders. Best-corrected visual acuity was 6/6p OU. Biomicroscopic examination of anterior segment was unremarkable OU. Fundus examination showed pigment clumps along the retinal vascular arcade with chorioretinal atrophy extending from the disc up to the equator with no involvement of the macula OU.

Complete blood count (CBC), erythrocyte sedimentation rate (ESR), C-reactive protein, and random blood sugar levels were within normal limits. Antinuclear antibody (ANA) test was negative and venereal disease research laboratory (VDRL) test was nonreactive.

OU fundus autofluorescence showed crescentic area of hyperfluorescence adjacent to area of chorioretinal atrophy. Full-field analysis showed peripheral field constriction OU. OCT revealed retinal thinning OU. ERG revealed reduced photopic and scotopic responses OU.

Learning Points:-
- The differential diagnoses of PPRCA include chorioretinal degeneration and inflammatory diseases that cause chorioretinal atrophy.

- The disease remains stationary in younger patients and slowly progress in older subjects.

- Currently, no specific treatment modality is available for PPRCA.

Know more here: https://pxmd.co/DxohN
Like
Comment
Share