Synovial sarcoma of kidney in a child: A rare presentation
Primary renal synovial sarcoma is an extremely rare disease with no reports in the pediatric population and few case reports in adults.[1,2,3] These tumors can be misdiagnosed as Wilms’ tumor, which is the most common renal malignancy in children. We report a case of primary renal synovial sarcoma in a child that mimicked Wilms’ tumor clinically and radiologically and discuss its management.
A 4-year-old female presented to our hospital with abdominal distension of 2 weeks duration. On examination, she had a right lumbar mass that was ballotable, normal blood pressure, and no dysmorphic feature. Computed tomographic (CT) scan of the abdomen showed an 11 × 8 cm mass arising from the upper pole of the right kidney [Figure 1]. The mass had both solid and cystic areas with calcification. There was a thrombus in the right renal vein extending along the inferior vena cava (IVC) till the right atrium. Her serum creatinine, urine routine examination, chest CT scan, and 24-h urine vanillylmandelic acid (VMA) levels were normal. Based on the clinical, radiological, and laboratory parameters a diagnosis of nonmetastatic Wilms’ tumor of the right kidney was made. ...
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