The tailor-made treatment in a particular case of pulmonary
Pulmonary hypertension (PH) is a haemodynamic condition, secondary to different causes. Thalassaemia may lead to PH of different origin and needs a comprehensive analysis to be correctly characterized and possibly treated.

Authors present a case study of a patient with a non-transfusion-dependent thalassaemia and a previous diagnosis of group 5 PH. A complete diagnostic assessment led to a specific diagnosis of chronic thromboembolic PH. Thus, they were able to start a specific therapy with riociguat that provided an improvement in terms of haemodynamic, imaging, and functional status.

A correct characterization and treatment of PH are essential in order to change the patient’s prognosis. Chronic thromboembolic PH is a treatable cause of PH in thalassemic patients and should be investigated.

Source: https://academic.oup.com/ehjcr/article/5/6/ytab193/6300012
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