Total Anomalous Systemic Venous Drainage with Heterotaxia Sy
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Introduction
Total anomalous systemic venous return is a very rare anomaly, where vena cava inferior (IVC), vena cava superior (SVC), and coronary sinus drain into left atrium [1]. In this report, we present a case of left atrial isomerism with anomalous systemic venous drainage, in a 2-day-old male patient. There are few published reports regarding the total anomalous systemic venous drainage with heterotaxy syndrome.

Case Report
Physical examination of the baby, who had postnatal cyanosis and tachypnea, was normal. Saturation was 70 percent in room air and cyanosis persisted, although oxygen therapy was started. Electrocardiography and chest X-ray were normal. On echocardiographic examination, the following findings were noted: interrupted IVC was present with left sided azygos continuation: azygos vein was draining into left SVC (Figure 1, see Supplementary Video??2); right SVC was absent; and left SVC was draining into left sided atrium via completely unroofed coronary sinus (see Supplementary Video 3)....

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4145383/
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