Tuberous sclerosis associated with multiple hepatic lipomato
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Tuberous sclerosis is a genetic multisystem disorder characterised by widespread hamartomas in several organs, including brain, heart, skin, eyes, kidney, lung and liver. Hepatic multiple angiomyolipomas (AML’s) are a rare and usually asymptomatic complication in patients with tuberous sclerosis.

Case presentation:
This article reports a 15-year-old girl with tuberous sclerosis who was noted to have multiple AML’s of the liver and kidneys found on routine ultrasound screening. She was asymptomatic at this stage and in view of the small size of the AML’s a repeat ultrasound of the liver and kidneys was performed twelve months later.
This showed a dramatic increase in the size of the AML’s. The patient was asymptomatic and had normal liver biochemistry and clotting. MRI of the liver showed signal dropout on opposed-phase imaging and also on spectral fat suppression, in keeping with fat content of the AML’s.These findings on MRI of the liver were typical of AML’s...

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