Congenital venolobar syndrome, pulmonary sequestration, and
Congenital pulmonary venolobar syndrome is a type of partial anomalous pulmonary venous return in which the affected lung is hypoplastic and is drained by an anomalous vein into the systemic venous system. Pulmonary sequestration is the aberrant formation of lung tissue that has no connection to the bronchial tree or pulmonary arteries. A horseshoe lung represents a band of pulmonary parenchyma extending between the right and left lungs. Presented here is a situation in which all 3 conditions manifest in concert.

At 6 days of life, an infant presented to cardiology clinic due to tachypnea. The tachypnea was initially only observed during feedings in the first few days of life, but it worsened and became apparent more regular. A chest radiograph was performed that showed a hypoplastic right lung with mediastinal shift to the right and pulmonary vascular congestion of the left lung.

A cardiac computed tomography performed during the second week of life showed 2 anomalous veins draining into the inferior vena cava. A well-defined pulmonary sequestration was apparent in the right lower lobe. The pulmonary sequestration was fed by an arterial branch from the aorta. Lung tissue was continuous across the inferior mediastinum in a horseshoe configuration.

Source: Radiology case reports

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