Multisystem Radiologic Manifestations of Erdheim-Chester Dis
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Erdheim-Chester Disease is a rare form of multiorgan non-Langerhans' cell histiocytosis that affects individuals between the ages of 50 and 70 with an equal distribution among males and females. It is associated with significant morbidity and mortality that is mostly due to infiltration of critical organs. Some of the sites that Erdheim-Chester Disease affects include the skeletal system, central nervous system, cardiovascular system, lungs, kidneys (retroperitoneum), and skin.

The most common presenting symptom of Erdheim-Chester Disease is bone pain although a large majority of patients are diagnosed incidentally during a workup for a different disease process. Diagnosing Erdheim-Chester Disease is challenging due its rarity and mimicry to other infiltrative processes. Therefore, a multimodality diagnostic approach is employed with imaging being at the forefront. As of date, a comprehensive radiologic review of the manifestations of Erdheim-Chester Disease has rarely been reported. Here we present radiologic findings of an individual suffering from Erdheim-Chester Disease.

Case Report
This patient is a 35-year-old male with no significant past medical history who presented to the emergency department with symptoms of “redness and swelling in his eyes associated with purulent discharge” that had failed to improve on outpatient antibiotic regimen. On further history, patient revealed that for about a year and a half, he had been experiencing grittiness and a “bulging” feeling in his eyes that he thought were due to seasonal allergies as well as loss of balance when standing or walking.