Successful epidural anesthesia in a patient of Hurler syndro
Mucopolysaccharidosis (MPS) is a rare inherited lysosomal storage diseases associated with progressive accumulation of glucosaminoglycans (GAGs) in tissues and organs. Surgery and anesthesia in these patients are associated with high mortality.1 The most serious anesthetic complications are associated with airway obstruction, with accompanying difficulty in ventilation and oxygenation, resulting in significant cardiovascular compromise. We describe a case of mucopolysaccharidosis type I (Hurler syndrome) for repair of umbilical and inguinal hernia repair conducted under epidural anesthesia with sedation, obviating the need of intubation.

A 4 year old, 12 kg, boy presented for umbilical and bilateral inguinal hernia repair (Figure 1). A known case of Hurler syndrome, he had a history of snoring, delayed developmental milestones and mental retardation.,,,